WILMS TUMOUR
by Atul Mishra

1. WT1 GENE(CHROMOSOME 11p13
1.1. WAGR
1.1.1. ANIRIDIA
1.1.2. RETARDATION MENTAL
1.1.3. GENITAL DYSGENESIS
1.2. DENYS -DRASH SYNDROME(DDS)
1.2.1. GONADAL DYSGENESIS
1.2.2. RENAL ABNORMALITIES
2. ABNORMALITY IN GENETIC IMPRINTING; CHROMOSOME 11 DISTAL TO WT1 LOCI
2.1. BECKWITH WIDDEMAN SYNDROME
2.1.1. ENLARGEMENT OF ORGANS LIKE MACROGLOSSIA
2.1.2. HEMIHYPERTROPHY