Types of Primary Immunodeficiency disorders

1. Humoral Immunodeficiencies ( B cell Defects)

1.1. 1. X-linked agammaglobulinemia

1.1.1. 2. Transient hypogammaglobulinemia of infancy

1.1.1.1. 3. Common variable immunodeficiency

1.1.1.1.1. 4. Selective immunoglobulin deficiencies

2. Cellular Immunodeficiencies ( T cell Defects)

2.1. Thymic Hypoplasia (DiGeorge's Syndrome)

3. Combined Immunodeficiencies (Both B & T cell Defects)

3.1. 1. Cellular immunodeficiency with abnormal Ig synthesis (Nezelof's Syndrome)

3.1.1. 2. Ataxia Telangiectasia

3.1.1.1. 3. Wiskott-Aldrich Syndrome

3.1.1.1.1. 4. Immunodeficiency with Thymoma

4. Disorders of Complement

4.1. 1. Complement component deficiencies

4.1.1. 2. Complement Inhibitor deficiencies

5. Disorders of Phagocytosis

5.1. 1. Chronic Granulomatous disease (CGD)

5.1.1. 2. Myeloperoxidase deficiency

5.1.1.1. 3. Chediak-Higashi Syndrome

5.1.1.1.1. 4. Jobs Syndrome